Banti's syndrome: case report and review of literature.

نویسندگان

  • S N Waqar
  • S Jindani
  • N S Baig
  • M A Waqar
  • F W Ismail
  • M Tariq
چکیده

In 1898 Banti described a disorder characterized by splenomegaly and hypersplenism, resulting in portal hypertension and anemia in the absence of hematological disease. 1 Banti's syndrome is also known as non-cirrhotic portal hypertension (NCPH) in India and Idiopathic Portal Hypertension (IPH) in Japan. Hepatoportal sclerosis seems to be its counterpart in the United States. 2,3 Banti's syndrome is a disorder of unknown etiology, clinically characterized by portal hypertension (varices and portosystemic collateral vessels), splenomegaly, and anemia (hypersplenism). 3 It has been reported from Indian subcontinent. 4-6 In a Pakistani case series of portal hypertension, 18 out of 37 patients were found to have IPH as the etiology. 6 We report a case of Banti's syndrome in an 20year old girl presenting to us with anemia and splenomegaly.

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عنوان ژورنال:
  • JPMA. The Journal of the Pakistan Medical Association

دوره 54 2  شماره 

صفحات  -

تاریخ انتشار 2004